2-Methylacetoacetyl-CoA

October 2026 changed 477214420 2-methylaceto-acetyl-CoA.png 250px 3′-O-Phosphonoadenosine 5′-[(3R)-3-hydroxy-2,2-dimethyl-4-({3-[(2-{[(2Ξ)-2-methyl-3-oxobutanoyl]sulfanyl}ethyl)amino]-3-oxopropyl}amino)-4-oxobutyl dihydrogen diphosphate] O1-{[(2R,3S,4R,5R)-5-(6-Amino-9H-purin-9-yl)-4-hydroxy-3-(phosphonooxy)oxolan-2-yl]methyl} O3-[(3R)-3-hydroxy-2,2-dimethyl-4-({3-[(2-{[(2Ξ)-2-methyl-3-oxobutanoyl]sulfanyl}ethyl)amino]-3-oxopropyl}amino)-4-oxobutyl] dihydrogen diphosphate correct chemspider 17216071 1/C26H42N7O18P3S/c1-13(14(2)34)25(39)55-8-7-28-16(35)5-6-29-23(38)20(37)26(3,4)10-48-54(45,46)51-53(43,44)47-9-15-19(50-52(40,41)42)18(36)24(49-15)33-12-32-17-21(27)30-11-31-22(17)33/h11-13,15,18-20,24,36-37H,5-10H2,1-4H3,(H,28,35)(H,29,38)(H,43,44)(H,45,46)(H2,27,30,31)(H2,40,41,42)/t13?,15-,18-,19-,20-,24-/m1/s1 NHNODHRSCRALBF-JGCWONBBBK correct chemspider 1S/C26H42N7O18P3S/c1-13(14(2)34)25(39)55-8-7-28-16(35)5-6-29-23(38)20(37)26(3,4)10-48-54(45,46)51-53(43,44)47-9-15-19(50-52(40,41)42)18(36)24(49-15)33-12-32-17-21(27)30-11-31-22(17)33/h11-13,15,18-20,24,36-37H,5-10H2,1-4H3,(H,28,35)(H,29,38)(H,43,44)(H,45,46)(H2,27,30,31)(H2,40,41,42)/t13?,15-,18-,19-,20-,24-/m1/s1 correct chemspider NHNODHRSCRALBF-JGCWONBBSA-N changed ?? 6712-01-2 53 CC(=O)[C@H](C)C(=O)SCCNC(=O)CCNC(=O)[C@@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]3O[C@@H](n2cnc1c(N)ncnc12)[C@H](O)[C@@H]3OP(O)(O)=O 2-methylacetoacetyl-coenzyme+A C26H42N7O18P3S 865.63 g/mol 2-Methylacetoacetyl-CoA is an intermediate in the metabolism of isoleucine. It was first synthesized n 1983.140 https://books.google.com/books?id=MjRpBQAAQBAJ&pg=PA140&dq=%222-Methylacetoacetyl-CoA%22+-wikipedia&hl=en&newbks=1&newbks_redir=0&source= Branched Chain Amino Acids in Clinical Nutrition, Volume 1, Chapter 11: Branched Chain Amino Acid Oxidation Disorders Ronald J.A. Wanders 2014 Springer New York 9781493919239 October 3, 2026 There is an extremely rare metabolic disorder, which involves humans who can't produce the enzyme that metabolizes the chemical into isoleucine; an emergency infusion of electrolytes and long-term a low-protein diet resolves the symptoms.282-285 https://books.google.com/books?id=Ka7yCAAAQBAJ&pg=PA283&dq=%222-Methylacetoacetyl-CoA%22+-wikipedia&hl=en&newbks=1&newbks_redir=0&source= Organic Acids in Man: Analytical Chemistry, Biochemistry and Diagnosis of the Organic Acidurias R. Chalmers A. M. Lawson 2012 Springer Netherlands 9789400957787 October 3, 2026102-108 Atlas of Metabolic Diseases Second Edition, Chapter 17 William L Nyhan Bruce A Barshop Pinar T. Ozand 2005 9780340809709 Taylor & Francis October 3, 2026 This condition is similar to Phenylketonuria. See also 3-hydroxy-2-methylbutyryl-CoA dehydrogenase References Category:Thioesters of coenzyme A